投票結果


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第189回(2006年9月29日)

* 発表者診断    # 討論での主な対抗意見

1265 右腎腫瘍 (物部泰昌先生)
* Malignant rhaboid tumor 20
   陽性:Vimentin, AE1/AE3, CAM5.2,一部陽性:EMA, αSMA, HHF-35,
 陰性:Desmin, CD56, Myoglobin, NF, MyoD1, MIC-2, S100, HMB-45, CD34, BCL-2, Calretinin
  Clear cell sarcoma
  Nephroblastoma 5
   nephroblastic type, abortic type 1
   fetal rhabdomyomatous 1
  Rhabdomyosarcoma 1
  Renal cell carcinoma 1
   granular cell carcinoma
 
1266 偶然発見の肺小結節 (赤木制二先生)
  Minute meningiothelial-like nodule 10
  (=Chemodectoma)
   * Minute, multiple 1
  Minute meningiothelioid nodule 4
  Minute meningiothelial nodule 4
  Adenocarcinoma with chemodectoma 1
  BAC mucinous type+chemodectoma 3
  Pericyte heperplasia in BAC 1
  Tumolet 1
  Carcinoid tumor 1
  Glomoid tumor 1
  Masson body 1
  IDK 1
 
1267 右下腿軟部腫瘍 (村尾 烈先生)
  Malignant peripheral nerve sheath tumor 14
  Extragastrointestinal stromal tumor (GIST) 1
  GIST-type stromal tumor 1
  Malignant triton tumor 1
  Rhabdomyosarcoma 1
  Leiomyosarcoma 1
  Synovial sarcoma 1
  Round cell liposarcoma 1
  Ewing sarcoma 1
* Sarcoma, high-grade 1
   診断するためには分子レベルの検索が必要。
 患者は岡大に転院してその後、岡大での検索は滑膜肉腫の融合遺伝子は検出されず。未だ、診断つかず。
IDK 1
 
1268 陰嚢腫瘍 (川端健二先生)  
  Leiomyosarcoma 21
*  + Osteosarcoma 1
   caldesmon(+), desmin(+)だが,再発部位では類骨形成あり→OS
 Low-grade LSからhigh-grade(pleomorphic) LSへと変化し,さらにOSへ。表層型LSでもhigh-gradeのものは要注意
 AJSP 25:1143-,2001   Virchows Arch 448:85-,2006   Histopathology 46:111-,2005.
  Liposarcoma, dedifferentiated 2
  Epithelioid sarcoma 1
  Extraskeletal osteosarcoma 1
  Embryonal rhabdomyosarcoma 1
  Undifferentiated pleomorphic sarcoma 1
  Mesothelioma 1
  Schwannoma with angiosarcoma 1
  Sex-cord tumor 1
 
1269 脳室内腫瘍 (三宅孝佳先生)
* Central neurocytoma 23
   NSE・Synaptphysinともに陽性
   vs. Clear cell ependymoma 1
  Neurocytoma 1
  Ependymoma, clear cell 3
   increased anaplasia 1
  Anaplastic ependymoma 1
  Oligodendroglioma 2
   grade II 1
1270 左鼠径リンパ節病変 (定平吉都先生)
  Malignant lymphoma 18
   diffuse large cell, immunoblastic 4
   diffuse large B-cell 3
   non-Hodgkin 3
   ALK positive 1
  Anaplastic large cell lymphoma, primary cutaneous 2
  Granulocytic sarcima 5
   myeloid sarcoma 1
  Plasmacytoma 1
  Lymph node invasion of mycosis fungoides / Sezary syndrome 1
  Malignant melanoma, metastatic 1
* IDK 1
   陽性: CD3ε, CD43, CD45, CD45RA, CD74,bcl-2, vimentin, 少数陽性:TdT
 陰性: κ, λ, CD15, CD20, CD30, CD34, CD56, CD68 (KP-1, PG-M1), Ki-M1p, CDw75, S100, TIA-1, cyclinD1, EMA, Myeloperoxidase lysozyme
 鑑別:Myeloid sacroma?or Dendritic precuror cell tumor
 Bone marrowへの再発なく,悪性リンパ腫の治療で12年間の再発なし。